Síndrome de Dyke-Davidoff-Masson: hallazgos radiológicos en un caso de hemiatrofia cerebral izquierda en adulto joven

Leonardo  Romero-Arnedo; Jefferson Jaimes-Bautista; Diana Hernández-Muñoz; Fausto Orozco; Sergio Andrés Chacón-Salazar; Juan Carlos Salcedo-Martínez

Authors

Romero-Arnedo Leonardo Médico. Residente en Radiología e Imágenes Diagnósticas. Facultad de Medicina, Universidad del Sinú. Cartagena, Colombia. https://orcid.org/0009-0003-1631-4805
Jaimes-Bautista Jefferson Médico. Residente en Radiología e Imágenes Diagnósticas. Facultad de Medicina, Universidad del Sinú. Cartagena, Colombia. https://orcid.org/0000-0001-5042-9663
Hernández-Muñoz Diana Médico. Especialista en Epidemiologia Universidad Autónoma de Bucaramanga (UNAB), Bucaramanga, Colombia. https://orcid.org/0000-0002-9923-5840
Orozco Fausto Médico. Especialista en Radiología. Médico, Docente en Radiología e Imágenes diagnosticas Universidad del Sinú. Cartagena, Colombia. https://orcid.org/0009-0004-7331-8121
Chacón-Salazar Sergio Andrés Médico. Universidad Metropolitana de Barranquilla. Barranquilla, Colombia. https://orcid.org/0009-0009-8544-9408
Salcedo-Martínez Juan Carlos Médico Especialista en Radiología, Universidad Ciencias Médicas de La Habana. Cuba. https://orcid.org/0000-0002-4145-3706

Keywords:

Dyke-Davidoff-Masson syndrome, cerebral hemiatrophy, magnetic resonance imaging, seizures, brain atrophy, radiological findings, congenital neurological disorders

Abstract

DOI: https://doi.org/10.46296/gt.v8i16.0260

Abstract

Dyke-Davidoff-Masson syndrome (DDMS) is a rare cerebral malformation characterized by cerebral hemiatrophy associated with compensatory hypertrophy of the skull and ipsilateral paranasal sinuses. Clinical manifestations include seizures, contralateral hemiparesis, and cognitive delay. Diagnosis is established through magnetic resonance imaging (MRI), which reveals hallmark features such as unilateral cerebral atrophy, ex vacuo ventricular dilatation, skull thickening, and gliosis. We present the case of a young adult with nonspecific neurological symptoms and a history of childhood epilepsy, in whom MRI demonstrated findings consistent with Dyke-Davidoff-Masson syndrome.

Keywords: Dyke-Davidoff-Masson syndrome, cerebral hemiatrophy, magnetic resonance imaging, seizures, brain atrophy, radiological findings, congenital neurological disorders.

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References

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